lupus
-
Clinical features •Rare cutaneous lymphoma with a generally good prognosis except for patients who develop a hemophagocytosis syndrome •2F:1M •Wide age range, can affect children & adolescents •Asymptomatic erythematous/violaceus nodules or deep plaques •Limbs & trunk but may be widespread •Variable B-symptoms in up to 50% of patients •Anemia, cytopenia, high ESR & abnormal liver function •Hemophagocytosis syndrome (20% of cases) •Coexistent autoimmune disease…